This study describes the outcomes of children with SBS by the multidisciplinary intestinal rehabilitation program (IRP) at the Sheffield Children’s Hospital A retrospective review of children with SBS on home parenteral nutrition between 2012 to 2021 using the Hospital electronic medical records.

A total of 23 patients with SBS were discharged on HPN. 14 were male and 9 were female. All except one presented in neonatal period. The aetiology in our cohort was gastroschisis (n 9%) followed by Necrotising enterocolitis (n 6%), volvulus (n 5%), intestinal atresia (n 2%), one was trichobezoar leading to intestinal perforation. The average small bowel length% length was 15.51%. 9 (39.1%) of our patients did not have ileo-caecal valve. 4(17%) patients underwent partial colectomy and 2(8.6)% underwent subtotal colectomy while 17 (73%) had a preserved colon. Intestinal continuity achieved in all except one patient. 5(21.7%) underwent gut lengthening procedure (STEP or Bianchi). 2 (8.6%) patients had IFALD%, d lactic acidosis in 6(26%) of our patients. 5(21.7%) had vitamin D deficiency and none had any trace element deficiencies. Overall, a full enteral autonomy was achieved in 17 (73.9%), parenteral nutrition dependent in 6 (26%), transplanted 3 (13%), one underwent isolated small bowel transplant, one combined bowel and liver and one isolated liver transplant (see table 1).

Survival of children with SBS was 100% and achieved excellent enteral autonomy with reduced morbidity secondary to complications under the guidance of IRP. Children with bowel length >30 cm achieved full enteral autonomy. Absence of ileo-caecal valve did not impact enteral autonomy in our group.